Description
4-Methylumbelliferyl-α- L-iduronic acid cyclohexylammonium salt is a fluorogenic soluble enzyme substrate for α-L-iduronidase. α-L-iduronidase is deficient in the genetic disorder Mucopolysaccharidosis type I, also called Hurler syndrome. 4-Methylumbelliferyl-α-L-iduronide is used in the diagnosis of Hurler syndrome as the substrate in an enzymatic assay of α-L-iduronidase activity.
Product Specifications
4-Methylumbelliferyl-α- L-iduronic acid cyclohexylammonium salt
4-Methylumbelliferyl-α-L-iduronide.
4-MU-α-L-IdoA • CHX
MOLECULAR BIOLOGY GRADE
Formula: C16H16O9 · C6H13N
MW: 451.48 g/mol
Storage/Handling: Store desiccated at -20°C. Protect from light.