Description
4-Methylumbelliferyl-α- L-iduronic acid cyclohexylammonium salt is a fluorogenic soluble enzyme substrate for α-L-iduronidase.  α-L-iduronidase is deficient in the genetic disorder  Mucopolysaccharidosis type I, also called Hurler syndrome. 4-Methylumbelliferyl-α-L-iduronide is used in the diagnosis of Hurler syndrome as the substrate in an enzymatic assay of α-L-iduronidase activity. 
 Product Specifications
4-Methylumbelliferyl-α- L-iduronic acid cyclohexylammonium salt 
 4-Methylumbelliferyl-α-L-iduronide. 
 4-MU-α-L-IdoA • CHX 
 MOLECULAR BIOLOGY GRADE 
  Formula: C16H16O9 · C6H13N 
 MW: 451.48 g/mol 
 Storage/Handling: Store desiccated at -20°C. Protect from light.